| Porphyrin biosynthesis | early mitochondrial: Aminolevulinic acid synthase (ALAS1, ALAS2) · Porphobilinogen synthase
cytosolic: Porphobilinogen deaminase · Uroporphyrinogen III synthase · Uroporphyrinogen III decarboxylase · Coproporphyrinogen III oxidase late mitochondrial: Protoporphyrinogen oxidase · Ferrochelatase | ||||
|---|---|---|---|---|---|
| Heme degradation to bile | |||||